Urological surgery in epidermolysis bullosa: tactical planning for surgery and anesthesia

AUTOR(ES)

Jesus, Lisieux Eyer de, Rangel, Maira, Moura Filho, Ronaldo S., Novaes, Glória, Quattrino, Ada, Aguas, Angelica F.

FONTE

Int. braz j urol.

DATA DE PUBLICAÇÃO

2014-10

RESUMO

Epidermolysis bullosa (EB) is characterized by extreme fragility of the skin and mucosae. Anesthetic and surgical techniques have to be adapted to those children and routine practice may not be adequate. Urological problems are relatively common, but surgical techniques adapted to those children have not been well debated and only low evidence is available to this moment. Herein we discuss the specifics of anesthetic and surgical techniques chosen to treat a six year old EB male presenting with symptomatic phimosis.

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