The case of a boy with nevus of Ota, extensive Mongolian spot, nevus flammeus, nevus anemicus and cutis marmorata telangiectatica congenita: a unique instance of phacomatosis pigmentovascularis
AUTOR(ES)
MA, Han, Liao, Mengsi, Qiu, Shu, Luo, Ruijun, Lu, Rongbiao, Lu, Chun
FONTE
An. Bras. Dermatol.
DATA DE PUBLICAÇÃO
2015-06
RESUMO
AbstractPhacomatosis pigmentovascularis is a rare, congenital condition characterized by a combination of cutaneous melanocytic lesions and vascular malformation. We discuss an entirely unique case of Phacomatosis pigmentovascularis with nevus of Ota, extensive Mongolian spot, nevus flammeus, nevus anemicus and cutis marmorata telangiectatica congenita, which may represent a heretofore undescribed variant of phacomatosis pigmentovascularis.
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