Síndrome de Prune Belly
AUTOR(ES)
Teixeira, Roni Leonardo, Petreca, Alexandre, Garcia, Patrícia Andréa Torres
FONTE
Revista do Colégio Brasileiro de Cirurgiões
DATA DE PUBLICAÇÃO
2004-12
RESUMO
Prune Belly Syndrome is a fetal uropathy of unknown etiology with incidence of 1/35000 to 1/50000 alive been born, characterized by a classical triad: abdominal musculature congenital deficiency, bilateral criptorquidia and urinary tract malformations. The authors present a case of this rare pathology associated with a patent urachus. After complementary exams confirmed urinary tract alterations (bilateral ureterohidronefrosis and vesicoureteral reflux degree 5, besides urinary infection), the surgical approach was vesicostomy to decrease urinary infections and sepsis. Definitve surgery should be accomplished around the 12th month of life. Nowadays, the child is asymptomatic , with follow-up every two months, with return consultation bimonthly.
Documentos Relacionados
- Abdominoplastia por plicatura anterior longitudinal na síndrome de prune belly: experiência inicial do hospital municipal Jesus
- Respiratory function in the prune-belly syndrome.
- Prune belly appearance in a Turner subject.
- Quantificação digital da imunoexpressão de receptores adrenérgicos e terminações nervosas no detrusor de portadores da síndrome de prune belly
- The prune belly anomaly: heterogeneity and superficial X-linkage mimicry.