Ofuji disease: a rare dermatosis and its challenging therapeutic approach

AUTOR(ES)

Brito, Fernanda Freitas de, Martelli, Antonio Carlos Ceribelli, Cavalcante, Maria Lopes Lamenha Lins, Pinto, Ana Cecília Versiani Duarte, Itimura, Gabriela, Soares, Cleverson Teixeira

FONTE

An. Bras. Dermatol.

DATA DE PUBLICAÇÃO

2016-10

RESUMO

Abstract: Eosinophilic pustular folliculitis (EPF) or Ofuji disease is a rare dermatosis, prone to recurrence and chronicity. The peak incidence occurs in the third decade of life and its exact etiology remains unknown. Evidence suggests that the expression of adhesion molecules and the production of cytokines activate the follicular unit, but the stimulus that triggers these changes remains unclear. The three clinical variants reported in the literature include classic EPF, immunosuppression-associated EPF, and infancy-associated EPF. We report a case of eosinophilic pustular folliculitis with peculiar epidemiological characteristics, which represents a challenging therapeutic scenario.

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