Non-classical forms of pemphigus: pemphigus herpetiformis, IgA pemphigus, paraneoplastic pemphigus and IgG/IgA pemphigus
AUTOR(ES)
Porro, Adriana Maria, Caetano, Livia de Vasconcelos Nasser, Maehara, Laura de Sena Nogueira, Enokihara, Milvia Maria dos Santos
FONTE
An. Bras. Dermatol.
DATA DE PUBLICAÇÃO
2014-01
RESUMO
The pemphigus group comprises the autoimmune intraepidermal blistering diseases classically divided into two major types: pemphigus vulgaris and pemphigus foliaceous. Pemphigus herpetiformis, IgA pemphigus, paraneoplastic pemphigus and IgG/IgA pemphigus are rarer forms that present some clinical, histological and immunopathological characteristics that are different from the classical types. These are reviewed in this article. Future research may help definitively to locate the position of these forms in the pemphigus group, especially with regard to pemphigus herpetiformis and the IgG/ IgA pemphigus.
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