Familial “benign” pemphigus? Erythroderma and fatal outcome,

AUTOR(ES)

Tansini, Paula Baldissera; Boff, Ana Letícia; Weber, Magda Blessmann; Bonamigo, Renan Rangel

FONTE

An. Bras. Dermatol.

DATA DE PUBLICAÇÃO

2020-02

RESUMO

Abstract Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome.

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